Rare Rheumatic Diseases of Immunologic Dysregulation

Description

This book is a practical, user-friendly guide for diagnosing and treating patients with rare rheumatic diseases of immunologic dysregulation. Covering uncommon diseases such as IgG4-Related Disease, Castleman’s Disease, and Felty Syndrome, chapters aggregate information from case reports and anecdotal literature to create a single, comprehensive handbook for treating patients. Each chapter provides historical perspective and epidemiology; a literature review (including research trials, translational research, historical and current case reports, and case series); pathogenesis; clinical presentation; laboratory evaluation; imaging; histopathology; treatment; and outcomes. Rare Rheumatic Diseases of Immunologic Dysregulation is an invaluable resource for rheumatologists, rheumatology fellows, and clinical immunologists to better diagnose and treat patients with rare rheumatic diseases. Front Matter ....Pages i-x Macrophage Activation Syndrome (Onyinye Iweala, Eveline Y. Wu)....Pages 1-25 Recurrent Fever Syndromes (Isabelle Jéru)....Pages 27-58 Common Variable Immunodeficiency (CVID) (Suzahn Ebert, Sonali Bracken, John Woosley, Kevin G. Greene, Jonathan Hansen, Leonard Jason Lobo et al.)....Pages 59-85 IgG4-Related Disease (Satomi Koizumi, Terumi Kamisawa, Sawako Kuruma, Kazuro Chiba, Masataka Kikuyama)....Pages 87-104 Relapsing Polychondritis (M. B. Adarsh, Aman Sharma)....Pages 105-119 Castleman’s Disease (Anne Musters, Sander W. Tas)....Pages 121-138 Remitting Seronegative Symmetrical Synovitis and Pitting Edema (Annemarie Schorpion, Reshmi Raveendran, Anupama Shahane, Mildred Kwan, Alfredo C. Rivadeneira)....Pages 139-155 Felty’s Syndrome (Jennifer Medlin, Rumey C. Ishizawar)....Pages 157-171 Back Matter ....Pages 173-178